2j9f
From Proteopedia
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- | [[Image:2j9f.jpg|left|200px]] | + | [[Image:2j9f.jpg|left|200px]] |
- | + | ||
- | '''HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE-DECARBOXYLASE E1B''' | + | {{Structure |
+ | |PDB= 2j9f |SIZE=350|CAPTION= <scene name='initialview01'>2j9f</scene>, resolution 1.88Å | ||
+ | |SITE= <scene name='pdbsite=AC1:Gol+Binding+Site+For+Chain+D'>AC1</scene> | ||
+ | |LIGAND= <scene name='pdbligand=MN:MANGANESE+(II)+ION'>MN</scene>, <scene name='pdbligand=K:POTASSIUM+ION'>K</scene>, <scene name='pdbligand=THV:C2-1-HYDROXY-3-METHYL-PROPYL-THIAMIN+DIPHOSPHATE'>THV</scene> and <scene name='pdbligand=GOL:GLYCEROL'>GOL</scene> | ||
+ | |ACTIVITY= [http://en.wikipedia.org/wiki/3-methyl-2-oxobutanoate_dehydrogenase_(2-methylpropanoyl-transferring) 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)], with EC number [http://www.brenda-enzymes.info/php/result_flat.php4?ecno=1.2.4.4 1.2.4.4] | ||
+ | |GENE= | ||
+ | }} | ||
+ | |||
+ | '''HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE-DECARBOXYLASE E1B''' | ||
+ | |||
==Disease== | ==Disease== | ||
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==About this Structure== | ==About this Structure== | ||
- | 2J9F is a [ | + | 2J9F is a [[Protein complex]] structure of sequences from [http://en.wikipedia.org/wiki/Homo_sapiens Homo sapiens]. Full crystallographic information is available from [http://oca.weizmann.ac.il/oca-bin/ocashort?id=2J9F OCA]. |
[[Category: 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)]] | [[Category: 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)]] | ||
[[Category: Homo sapiens]] | [[Category: Homo sapiens]] | ||
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[[Category: transit peptide]] | [[Category: transit peptide]] | ||
- | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Thu | + | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Thu Mar 20 17:39:01 2008'' |
Revision as of 15:39, 20 March 2008
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, resolution 1.88Å | |||||||
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Sites: | |||||||
Ligands: | , , and | ||||||
Activity: | 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring), with EC number 1.2.4.4 | ||||||
Coordinates: | save as pdb, mmCIF, xml |
HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE-DECARBOXYLASE E1B
Disease
Known disease associated with this structure: Maple syrup urine disease, type Ia OMIM:[608348]
About this Structure
2J9F is a Protein complex structure of sequences from Homo sapiens. Full crystallographic information is available from OCA.
Page seeded by OCA on Thu Mar 20 17:39:01 2008
Categories: 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) | Homo sapiens | Protein complex | Chuang, D T. | Chuang, J L. | Jun, L. | Machius, M. | Wynn, R M. | GOL | K | MN | THV | Branched-chain | Disease mutation | Flavoprotein | Ketoacid dehydrogenase | Maple syrup urine disease | Metal-binding | Mitochondrion | Multi-enzyme complex | Oxidoreductase | Phosphorylation | Potassium | Thiamine pyrophosphate | Transit peptide