2j9f
From Proteopedia
(Difference between revisions)
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|PDB= 2j9f |SIZE=350|CAPTION= <scene name='initialview01'>2j9f</scene>, resolution 1.88Å | |PDB= 2j9f |SIZE=350|CAPTION= <scene name='initialview01'>2j9f</scene>, resolution 1.88Å | ||
|SITE= <scene name='pdbsite=AC1:Gol+Binding+Site+For+Chain+D'>AC1</scene> | |SITE= <scene name='pdbsite=AC1:Gol+Binding+Site+For+Chain+D'>AC1</scene> | ||
- | |LIGAND= <scene name='pdbligand= | + | |LIGAND= <scene name='pdbligand=GOL:GLYCEROL'>GOL</scene>, <scene name='pdbligand=K:POTASSIUM+ION'>K</scene>, <scene name='pdbligand=MN:MANGANESE+(II)+ION'>MN</scene>, <scene name='pdbligand=THV:C2-1-HYDROXY-3-METHYL-PROPYL-THIAMIN+DIPHOSPHATE'>THV</scene> |
- | + | |ACTIVITY= <span class='plainlinks'>[http://en.wikipedia.org/wiki/3-methyl-2-oxobutanoate_dehydrogenase_(2-methylpropanoyl-transferring) 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)], with EC number [http://www.brenda-enzymes.info/php/result_flat.php4?ecno=1.2.4.4 1.2.4.4] </span> | |
|GENE= | |GENE= | ||
+ | |DOMAIN= | ||
+ | |RELATEDENTRY= | ||
+ | |RESOURCES=<span class='plainlinks'>[http://oca.weizmann.ac.il/oca-docs/fgij/fg.htm?mol=2j9f FirstGlance], [http://oca.weizmann.ac.il/oca-bin/ocaids?id=2j9f OCA], [http://www.ebi.ac.uk/pdbsum/2j9f PDBsum], [http://www.rcsb.org/pdb/explore.do?structureId=2j9f RCSB]</span> | ||
}} | }} | ||
'''HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE-DECARBOXYLASE E1B''' | '''HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE-DECARBOXYLASE E1B''' | ||
- | |||
- | ==Disease== | ||
- | Known disease associated with this structure: Maple syrup urine disease, type Ia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=608348 608348]] | ||
==About this Structure== | ==About this Structure== | ||
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[[Category: Machius, M.]] | [[Category: Machius, M.]] | ||
[[Category: Wynn, R M.]] | [[Category: Wynn, R M.]] | ||
- | [[Category: GOL]] | ||
- | [[Category: K]] | ||
- | [[Category: MN]] | ||
- | [[Category: THV]] | ||
[[Category: branched-chain]] | [[Category: branched-chain]] | ||
[[Category: disease mutation]] | [[Category: disease mutation]] | ||
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[[Category: transit peptide]] | [[Category: transit peptide]] | ||
- | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on | + | ''Page seeded by [http://oca.weizmann.ac.il/oca OCA ] on Mon Mar 31 03:54:58 2008'' |
Revision as of 00:54, 31 March 2008
| |||||||
, resolution 1.88Å | |||||||
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Sites: | |||||||
Ligands: | , , , | ||||||
Activity: | 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring), with EC number 1.2.4.4 | ||||||
Resources: | FirstGlance, OCA, PDBsum, RCSB | ||||||
Coordinates: | save as pdb, mmCIF, xml |
HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE-DECARBOXYLASE E1B
About this Structure
2J9F is a Protein complex structure of sequences from Homo sapiens. Full crystallographic information is available from OCA.
Page seeded by OCA on Mon Mar 31 03:54:58 2008
Categories: 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) | Homo sapiens | Protein complex | Chuang, D T. | Chuang, J L. | Jun, L. | Machius, M. | Wynn, R M. | Branched-chain | Disease mutation | Flavoprotein | Ketoacid dehydrogenase | Maple syrup urine disease | Metal-binding | Mitochondrion | Multi-enzyme complex | Oxidoreductase | Phosphorylation | Potassium | Thiamine pyrophosphate | Transit peptide