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1olu
From Proteopedia
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caption="1olu, resolution 1.90Å" /> | caption="1olu, resolution 1.90Å" /> | ||
'''ROLES OF HIS291-ALPHA AND HIS146-BETA' IN THE REDUCTIVE ACYLATION REACTION CATALYZED BY HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE'''<br /> | '''ROLES OF HIS291-ALPHA AND HIS146-BETA' IN THE REDUCTIVE ACYLATION REACTION CATALYZED BY HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE'''<br /> | ||
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| + | ==Disease== | ||
| + | Known diseases associated with this structure: Maple syrup urine disease, type Ia OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=608348 608348]], Maple syrup urine disease, type Ib OMIM:[[http://www.ncbi.nlm.nih.gov/entrez/dispomim.cgi?id=248611 248611]] | ||
==About this Structure== | ==About this Structure== | ||
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[[Category: thiamine phosphate]] | [[Category: thiamine phosphate]] | ||
| - | ''Page seeded by [http://ispc.weizmann.ac.il/oca OCA ] on Mon Nov | + | ''Page seeded by [http://ispc.weizmann.ac.il/oca OCA ] on Mon Nov 12 18:34:31 2007'' |
Revision as of 16:28, 12 November 2007
|
ROLES OF HIS291-ALPHA AND HIS146-BETA' IN THE REDUCTIVE ACYLATION REACTION CATALYZED BY HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE
Disease
Known diseases associated with this structure: Maple syrup urine disease, type Ia OMIM:[608348], Maple syrup urine disease, type Ib OMIM:[248611]
About this Structure
1OLU is a Protein complex structure of sequences from Homo sapiens with K, MG, TDP and GOL as ligands. Active as 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring), with EC number 1.2.4.4 Structure known Active Site: KA. Full crystallographic information is available from OCA.
Page seeded by OCA on Mon Nov 12 18:34:31 2007
Categories: 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) | Homo sapiens | Protein complex | Chuang, D.T. | Chuang, J.L. | Li, J. | Machius, M. | Tomchick, D.R. | Wynn, R.M. | GOL | K | MG | TDP | Acylation | Branched-chain | Ketoacid dehydrogenase | Maple syrup urine disease | Multi-enzyme complex | Oxidative decarboxylation oxidoreductase | Thiamine phosphate
