1x7y
From Proteopedia
Contents |
Crystal structure of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase
Template:ABSTRACT PUBMED 15576032
Disease
Known disease associated with this structure: Maple syrup urine disease, type Ia OMIM:[608348], Maple syrup urine disease, type Ib OMIM:[248611]
About this Structure
1X7Y is a Protein complex structure of sequences from Homo sapiens. Full crystallographic information is available from OCA.
Reference
Molecular mechanism for regulation of the human mitochondrial branched-chain alpha-ketoacid dehydrogenase complex by phosphorylation., Wynn RM, Kato M, Machius M, Chuang JL, Li J, Tomchick DR, Chuang DT, Structure. 2004 Dec;12(12):2185-96. PMID:15576032
Page seeded by OCA on Tue Jul 29 00:59:37 2008
Categories: Homo sapiens | Protein complex | Chuang, D T. | Chuang, J L. | Kato, M. | Li, J. | Machius, M. | Tomchick, D R. | Wynn, R M. | Acylation | Branched-chain | Flavoprotein | Multi-enzyme complex | Oxidative decarboxylation maple syrup urine disease | Oxidoreductase,ketoacid dehydrogenase | Phosphorylation | Thiamin diphosphate